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A 66-year-old man with a long history of ulcerative colitis treated with azathioprine

66 years old | Male

Vignette:

A 66-year-old man with a long history of ulcerative colitis treated with azathioprine is found to have abnormal liver function tests. His bilirubin and ALT are normal but alkaline phosphatase is three times the upper limit of normal.

Summary:

history of ulcerative colitis | azathioprine | abnormal liver function tests | elevated alkaline phosphatase

Dx:

PSC

Ref:

ccu hepatology MCQ 8 page 168

Rank

Disease

Weight

1 Osteomalacia 195.0
2 Primary sclerosing cholangitis 181.0
3 Cholangiocarcinoma 163.0
4 Common cutaneous drug reactions 158.0
5 Mirizzi Syndrome 153.0
6 Autoimmune hepatitis 140.0
7 Amebic Liver Abscess 136.0
8 Extraintestinal Entamoeba histolytica amebiasis 136.0
9 Acute Cholangitis 134.0
10 Acalculous Cholecystitis 133.0
11 chronic acalculous cholecystitis 133.0
12 Klebsiella pneumoniae liver abscess 133.0
13 Acute Liver Failure 128.0
14 Pyogenic Liver Abscess 124.0
15 Choledocholithiasis 120.0
16 Amyloidosis 117.0
17 Primary biliary cirrhosis 115.0
18 Eclampsia 110.0
19 Autoimmune Pancreatitis 107.0
20 Acute heart failure 104.0
21 Budd Chiari Syndrome 103.0
22 Toxic Megacolon 101.0
23 Osteoporosis 100.0
24 Breast Cancer 100.0
25 Gastritis 96.0
26 Celiac Disease 95.0
27 Ulcerative Colitis 93.0
28 Crohn Disease 93.0
29 Cholestasis 88.0
30 Intrahepatic Cholestasis 88.0
31 Extrahepatic Cholestasis 88.0
32 Chronic Hepatitis 85.0
33 Gallbladder Dyskinesia 85.0
34 Non-small cell lung cancer 80.0
35 biliary SOD 78.0
36 Hyperthyroidism 78.0
37 Graves Disease 78.0
38 Hypogammaglobulinemia 76.0
39 Gallbladder cancer 74.0
40 Gallstones 72.0
41 Adrenocortical carcinoma 70.0
42 Hepatocellular carcinoma 64.0
43 Gallstone pancreatitis 64.0
44 Autosomal Recessive Polycystic Kidney Disease 64.0
45 Systemic lupus erythematosus 64.0
46 Acute Hepatitis 63.0
47 Cystic Fibrosis 62.0
48 Typhoid infection 62.0
49 Short bowel syndrome 61.0
50 Alcoholic hepatitis 57.0
51 Endometrial cancer 56.0
52 Alcoholic Fatty Liver 54.0
53 Acute viral meningitis 54.0
54 Chronic atrial fibrillation 54.0
55 chronic biliary obstruction 53.0
56 Biliary cirrhosis 53.0
57 Colorectal cancer 50.0
58 Herpes zoster 50.0
59 Type 1 Diabetes mellitus 50.0
60 biliary obstruction 50.0
61 Aseptic meningitis 50.0
62 Graves ophthalmopathy 49.0
63 Non-alcoholic Fatty Liver Disease 48.0
64 Kawasaki disease 48.0
65 Toxic thyroid adenoma 48.0
66 Chronic pelvic pain in women 47.0
67 Acute Cholecystitis 47.0
68 Acute Myeloid Leukemia in children 47.0
69 Sarcoidosis 45.0
70 Chronic Lymphocytic Leukemia 44.0
71 Lung Cancer 42.0
72 Primary Myelofibrosis 40.0
73 Liver Abscess 40.0
74 Hepatic Encephalopathy 39.0
75 Acetaminophen overdose 39.0
76 Oropharyngeal cancer 38.0
77 Goiter 37.0
78 Obstructive cervical goiters 37.0
79 Toxic multinodular goiter 37.0
80 Diffuse nontoxic goiter 37.0
81 Cervical goiter 37.0
82 Scleritis 36.0
83 Anterior scleritis 36.0
84 Posterior scleritis 36.0
85 Hereditary hemochromatosis 36.0
86 Intrahepatic cholestasis of pregnancy 36.0
87 Wilson disease 35.0
88 Chronic Cholecystitis 35.0
89 Chronic Clonorchiasis 35.0
90 Stevens-Johnson syndrome 34.0
91 Acute Pancreatitis 34.0
92 Chronic liver disease 34.0
93 Inflammatory Bowel Diseases 33.0
94 Glomerulonephritis 32.0
95 Clonorchiasis 31.0
96 Familial adenomatous polyposis syndrome 31.0
97 Deep venous thrombosis 30.0
98 Erythema nodosum 30.0
99 Clostridium difficile infection 30.0
100 Infertility in women 30.0
101 Fungal meningitis 30.0
102 Infectious mononucleosis 30.0
103 Peutz-Jeghers Syndrome 30.0
104 pericholangitis 30.0
105 Testicular cancer 27.0
106 Acute Lymphocytic Leukemia in Adults 27.0
107 Painless thyroiditis 27.0
108 Autosomal Dominant Polycystic Kidney Disease 27.0
109 Diverticulitis 27.0
110 Intra-abdominal abscess 26.0
111 Emphysematous cholecystitis 26.0
112 Renal and perinephric abscess 25.0
113 Gilbert syndrome 25.0
114 Psychogenic polydipsia 25.0
115 Malaria 24.0
116 Acute Clonorchiasis 23.0
117 Chronic heart failure 23.0
118 Hypothyroidism 22.0
119 Systemic sclerosis 22.0
120 Pulmonary Embolism 21.0
121 Liver Cirrhosis 20.0
122 Alcoholic Liver Disease 20.0
123 Alcoholic Liver Cirrhosis 20.0
124 Ovarian Hyperstimulation Syndrome 20.0
125 Preeclampsia 20.0
126 Familial Mediterranean fever 20.0
127 Hemolytic uremic syndrome 20.0
128 Prolactinoma 20.0
129 Hepatorenal Syndrome 18.0
130 Gestational diabetes mellitus 18.0
131 Tuberculous Peritonitis 18.0
132 Hyperprolactinemia 18.0
133 Hyperaldosteronism 18.0
134 Hyperparathyroidism 18.0
135 Osteomyelitis 18.0
136 Primary hypogonadism 18.0
137 Secondary hypogonadism 18.0
138 Acute fatty liver of pregnancy 17.0
139 Rheumatoid Arthritis 17.0
140 Acute intermittent porphyria 16.0
141 Menopause 16.0
142 Psoas Abscess 15.0
143 Rocky Mountain spotted fever 15.0
144 Epididymo-orchitis 14.0
145 pancreatic SOD 14.0
146 Brucellosis 14.0
147 Atypical pneumonia 14.0
148 Cushing syndrome 14.0
149 Salmonella infection 13.0
150 pancreatic cancer 13.0
151 Foodborne E coli infection 12.0
152 Chronic Pancreatitis 12.0
153 Hypertriglyceridemia 12.0
154 Hereditary Angioedema 11.0
155 Disseminated intravascular coagulation 11.0
156 Renal Cell Carcinoma 11.0
157 Food poisoning 11.0
158 Pancreatic Pseudocyst 11.0
159 Thrombotic thrombocytopenic purpura 11.0
160 Ankylosing spondylitis 8.0
161 Thyroid lymphoma 8.0
162 Anaplastic thyroid cancer 8.0
163 Annular pancreas 8.0
164 Hypercalcemia 8.0
165 Pseudohypoparathyroidism 8.0
166 Pneumonia 8.0
167 Acromegaly 7.0
168 Polyarteritis nodosa 6.0
169 Mesenteric ischemia 4.0
170 Non-ST-elevation myocardial infarction 4.0
171 Intestinal malrotation 3.0
172 Granulomatosis with polyangiitis 2.0
173 Alopecia areata 1.0
174 Irritable Bowel Syndrome 0.0
175 Abetalipoproteinemia 0.0
176 Bell palsy 0.0
177 Phenylketonuria 0.0
178 Immune thrombocytopenia 0.0