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Churg-Strauss Syndrome
Syn.
EGPA
, CSS allergic granulomatosis and angiitis
, Eosinophilic granulomatosis with polyangiitis
Signs & Symptoms
Nasal obstruction
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Omalizumab
Ref:
Uptodate
[
Epidemiology, pathogenesis, and pathology of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Montelukast
Ref:
Uptodate
[
Epidemiology, pathogenesis, and pathology of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Inhaled glucocorticoids
Ref:
Uptodate
[
Epidemiology, pathogenesis, and pathology of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Physical Examination
Pleural effusion
Note:
Can be discovered in chest radiography and pulmonary examination
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Wheezing
Note:
due to Asthma
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Tender nodules on the extensor surfaces of the hands
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Harrison
[
2582
]
Lab / Serology
Elevated ESR
Ref:
Harrison
[
2582
]
Elevated fibrinogen
Ref:
Harrison
[
2582
]
Elevated alpha-2 globulins
Ref:
Harrison
[
2582
]
Imagin Study
Transient pulmonary opacities
#Criteria
Note:
Without lobar or segmental distribution
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Migratory pulmonary opacities
#Criteria
Note:
Without lobar or segmental distribution
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Abnormal electrocardiogram
Ref:
Uptodate
[
Clinical features and diagnosis of eosinophilic granulomatosis with polyangiitis (Churg-Strauss)
]
Complication
Risk Factors
Cause
Other